Isifo seBrugada: yintoni, iimpawu kunye nendlela yonyango olwenziwe ngayo

Umxholo

• Iimpawu kunye neempawu
• Indlela yokuchonga
• Unyango lwenziwa njani

Isifo seBrugada sisifo sentliziyo esinqabileyo nesifuzelwa sisifo esibonakaliswa lutshintsho kwimisebenzi yentliziyo enokubangela iimpawu ezinje ngokuba nesiyezi, ukuphelelwa ngamandla nokuphefumla nzima, ukongeza ekubangeleni ukufa ngesiquphe kwezona meko zinzima. Esi sifo sixhaphake kakhulu emadodeni kwaye sinokwenzeka nangaliphi na ixesha ebomini.

I-Brugada syndrome ayinanyango, nangona kunjalo inokunyangwa ngokuqina kwaye ihlala ibandakanya ukumiliselwa kwe-cardiodefibrillator, esisixhobo esinoxanduva lokujonga kunye nokulungisa ukubetha kwentliziyo xa kukho ukufa ngesiquphe, umzekelo. Isifo iBrugada sichongwa ngugqirha wezifo zentliziyo ngokusebenzisa i-electrocardiogram, kodwa ke iimvavanyo zemfuzo zinokwenziwa ukujonga ukuba ngaba umntu lowo unoxanduva lwesifo na.

Iimpawu kunye neempawu

Isifo iBrugada sidla ngokungabi nazimpawu, nangona kunjalo, kuyinto eqhelekileyo ukuba umntu onale syndrome abe nesiyezi, aphelelwe ngamandla okanye aphefumle nzima. Ukongeza, luphawu lwesi sifo ukuba imeko eqatha ye-arrhythmia, apho intliziyo inokubetha kancinci, ngaphandle kwesingqisho okanye ngokukhawuleza, nto leyo edla ngokwenzeka. Ukuba le meko ayinyangwa, inokukhokelela ekufeni ngequbuliso, imeko leyo ebonakaliswa kukungapomfi kwegazi emzimbeni, okukhokelela ekuphelelweni kukungabikho kokubetha nokuphefumla. Jonga ukuba zeziphi izizathu eziphambili zokufa ngesiquphe.

Indlela yokuchonga

I-Brugada syndrome ixhaphake kakhulu kubantu abadala, kodwa inokwenzeka nanini na ebomini kwaye inokuchongwa ngoku:

• I-Electrocardiogram (ECG), apho ugqirha aya kuvavanya umsebenzi wombane wentliziyo ngokuchaza iigrafu ezenziwe ngesixhobo, akwazi ukuqinisekisa isingqisho kunye nenani lokubetha kwentliziyo. Isifo iBrugada sineeprofayili ezintathu kwi-ECG, kodwa kukho iprofayili ethe rhoqo enokuthi ivale ukufumanisa isifo. Qonda ukuba yeyantoni kwaye yenziwa njani i-electrocardiogram.
• Ukukhuthaza iziyobisi, apho kunokusetyenziswa sisigulana iyeza elinakho ukutshintsha umsebenzi wentliziyo, onokuthi uqondwe nge-electrocardiogram. Ngokwesiqhelo iyeza elisetyenziswa yi-cardiologist ngu-Ajmalina.
• Uvavanyo lwemfuzo okanye iingcebiso, kuba sisifo esifa, kulindelekile ukuba utshintsho olwenzeka kwisifo lubekhona kwi-DNA, kwaye lunokuchongwa ngovavanyo oluthile lweemolekyuli. Ukongeza, ingcebiso ngemfuza inokwenziwa, apho ithuba lokuvela kwesi sifo liqinisekisiweyo. Jonga ukuba loluphi ululeko ngofuzo.

Isifo iBrugada asinyangeki, yimeko yemfuza kunye nelifa, kodwa kukho iindlela zokuthintela ukuqala, njengokuthintela ukusetyenziswa kotywala kunye namayeza anokukhokelela kwisifo, umzekelo.

Unyango lwenziwa njani

Xa umntu esemngciphekweni omkhulu wokufa ngesiquphe, kuhlala kucetyiswa ngugqirha ukuba abeke isixhobo se-cardioverter defibrillator (ICD), esisisixhobo esifakwe phantsi kwesikhumba esinoxanduva lokujonga izingqi zentliziyo kunye nokukhuthaza ukusebenza kwentliziyo xa kuphazamisekile.

Kwiimeko ezinobulali, apho ithuba lokufa ngesiquphe liphantsi, ugqirha unokucebisa ngokusetyenziswa kwamayeza, afana nequinidine, umzekelo, enomsebenzi wokuthintela ezinye iimpahla zentliziyo kunye nokunciphisa inani lezicatshulwa, kuba iluncedo kunyango lwe-arrhythmias, umzekelo.