Ikhupha kabini i-ventricle yasekunene

Ukuphuma kabini kwi-ventricle yasekunene (i-DORV) sisifo sentliziyo esivela ekuzalweni (kwento yokuzalwa). I-aorta iqhagamshela kwi-ventricle elungileyo (i-RV, igumbi lentliziyo elipompa igazi elingenayo i-oxygen kwimiphunga), endaweni ye-ventricle yasekhohlo (i-LV, igumbi elihlala lipompa igazi eline-oksijini emzimbeni).

Zombini i-pulmonary artery (ethwala ioksijini-engenagazi kwimiphunga) kunye ne-aorta (ethwala ioksijini enegazi elityebileyo isuka entliziyweni iye emzimbeni) ivela kwigumbi elinye lokumpompa. Akukho mithetho iqhagamshelwe kwi-ventricle yasekhohlo (kwigumbi elihlala lipompa igazi emzimbeni).

Kwindlela eqhelekileyo yokwakheka kwentliziyo, i-aorta iqhagamshela kwi-LV. Umthambo we-pulmonary ngesiqhelo uqhagamshelwe kwi-RV. Kwi-DORV, yomibini imithambo ephuma kwi-RV. Le yingxaki kuba iRV ithwala igazi elingena oxygen. Eli gazi ke lijikeleza emzimbeni wonke.

Esinye isiphene esibizwa ngokuba sisiphene se-ventricular septal (VSD) sihlala sisenzeka nge-DORV.

Igazi elinobutyebi be-oksijini kwimiphunga liphuma kwicala lasekhohlo lentliziyo, ngokuvulwa kwe-VSD nakwi-RV. Oku kunceda usana olune-DORV ngokuvumela igazi eline-oksijini exutywe negazi elingena-oxygen. Nokuba unalo mxube, umzimba unokungafumani oksijini yaneleyo. Oku kwenza ukuba intliziyo isebenze nzima ukuhlangabezana neemfuno zomzimba. Kukho iindidi ngeendidi zeDORV.

Umahluko phakathi kwezi ntlobo yindawo ye-VSD njengoko inxulumene nendawo ye-pulmonary artery kunye ne-aorta. Iimpawu kunye nobukhulu bengxaki buya kuxhomekeka kuhlobo lwe-DORV. Ubukho be-valve stenosis ye-pulmonary nayo ichaphazela imeko.

Abantu abane-DORV bahlala benezinye iziphene zentliziyo, ezinje:

• Iziphene ze-Endocardial cushion (iindonga ezahlula onke amagumbi amane entliziyo azenziwanga kakuhle okanye azikho)
• Ukudibanisa i-aorta (ukunciphisa i-aorta)
• Iingxaki zevalve zeMitral
• I-pulmary atresia (i-valve yemiphunga ayifaki kakuhle)
• I-valve stenosis ye-pulmonary (ukunciphisa i-valve ye-pulmonary valve)
• I-aortic arch esecaleni lasekunene (i-aortic arch isekunene endaweni yasekhohlo)
• Ukutshintshwa kweemithambo ezinkulu (i-aorta kunye ne-pulmonary artery itshintshiwe)

Iimpawu ze-DORV zinokubandakanya:

• Yandisa intliziyo
• Ukumbombozela kwentliziyo
• Ukuphefumla ngokukhawuleza
• Ukubetha kwentliziyo okukhawulezayo

Iimpawu ze-DORV zinokubandakanya:

• Ukutya okungalunganga ngenxa yokudinwa ngokulula
• Umbala oluhlaza okwesibhakabhaka kunye nemilebe
• Iiklabhu (ukuqina kweebhedi zezikhonkwane) zeenzwane neminwe (uphawu lwasemva kwexesha)
• Ukusilela ukutyeba kunye nokukhula
• Umbala omdaka
• Ukubila
• Imilenze idumbile okanye isisu
• Ingxaki yokuphefumla

Uvavanyo lokufumanisa i-DORV lubandakanya:

• I-X-ray yesifuba
• Uvavanyo lwe-Ultrasound lwentliziyo (i-echocardiogram)
• Ukugqithisa ityhubhu ebhityileyo, eguqukayo ungene entliziyweni ukulinganisa uxinzelelo lwegazi kunye nokujova idayi yemifanekiso ekhethekileyo yentliziyo kunye nemithambo (catheterization yentliziyo)
• I-MRI yentliziyo

Unyango lufuna utyando ukuvala umngxuma osentliziyweni kunye nokuhambisa igazi ukusuka kwi-ventricle yasekhohlo iye kwi-aorta. Utyando lunokufuneka kwakhona ukuhambisa umthambo we-pulmonary okanye i-aorta.

Izinto ezichonga uhlobo kunye nenani lokusebenza kwezinto ezifunwa ngumntwana zibandakanya:

• Uhlobo lwe-DORV
• Ubunzima besiphene
• Ubukho bezinye iingxaki entliziyweni
• Imeko yomntwana iyonke

Indlela aqhuba ngayo umntwana ixhomekeke:

• Ubungakanani kunye nendawo ye-VSD
• Ubungakanani bamagumbi okupompa
• Indawo ye-aorta kunye ne-pulmonary artery
• Ubukho bezinye iingxaki (ezinje ngokujikeleza kwe-aorta kunye ne-mitral valve iingxaki)
• Impilo yomntwana ngokubanzi ngexesha lokuxilongwa
• Nokuba umonakalo wemiphunga wenzekile kwigazi elininzi elibalekela emiphungeni ixesha elide

Iingxaki ezivela kwi-DORV zinokubandakanya:

• Ukumelwa yintliziyo
• Uxinzelelo lwegazi oluphezulu emiphungeni, olunganyangekiyo lungakhokelela kumonakalo osisigxina wemiphunga
• Ukufa

Abantwana abanesi simo sentliziyo banokufuna ukuthatha ii-antibiotics ngaphambi konyango lwamazinyo. Oku kuthintela usulelo olujikeleze intliziyo. Amayeza okubulala iintsholongwane nawo anokufuneka emva kotyando.

Fowunela umboneleli wakho wezempilo ukuba umntwana wakho ubonakala edinwa ngokulula, enengxaki yokuphefumla, okanye enesikhumba esimnyama okanye imilebe. Kuya kufuneka unxibelelane nomboneleli wakho ukuba umntwana wakho akakhuli okanye akazinzi.

IDORV; Ukungalingani kweTaussig-Bing; I-DORV ene-VSD ezibophelele kabini; I-DORV nge-VSD engazibophelelanga; I-DORV ene-subaortic VSD; Isiphene sentliziyo esibelekwe - iDORV; Isiphene sentliziyo yeCyanotic - iDORV; Isiphene sokuzalwa-DORV

• Ikhupha kabini i-ventricle yasekunene

UBichell D. Ukuphinda kabini ukuphuma kwivenkile elungileyo. Ku: Ungerleider RM, Meliones JN, McMillian KN, Cooper DS, Jacobs JP, ii-eds. Isifo sentliziyo esibalulekileyo kwiintsana nasebantwaneni. Ngomhla wesi-3. IPhiladelphia, PA: Elsevier; I-2019: isahluko 58.

IHallerle C, uVan Arsdell GS, uYoo SJ, uGeorge-Hyslop CST, uSpicer DE, kunye noAnderson A. Ku: Wernovsky G, Anderson RH, Kumar K, et al. Anderson's Cardiology yabantwana. Ngomhla we-4. IPhiladelphia, PA: Elsevier; 2020: isahluko 39.

IWebb GD, i-Smallhorn JF, iTherrien J, iRedington AN. Isifo sentliziyo esibelekwe kumntu omkhulu nakwisigulana sabantwana. Ku: Zipes DP, Libby P, Bonow RO, Mann DL, Tomaselli GF, Braunwald E, ii-eds. Isifo sentliziyo seBraunwald: Incwadi yesifundo seMpilo yeNtliziyo. Ngomhla we-11. IPhiladelphia, PA: Elsevier; I-2019: isahluko 75.